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CASE REPORT
Year : 2018  |  Volume : 5  |  Issue : 1  |  Page : 63-66

A rare case of severe Hunter's Syndrome


Department of Pedodontia and Preventive Dentistry, Christian Dental College, Ludhiana, Punjab, India

Correspondence Address:
Sharon Vincent
Department of Pedodontia and Preventive Dentistry, Christian Dental College, Brown Road, Ludhiana - 141 008, Punjab
India
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Source of Support: None, Conflict of Interest: None


DOI: 10.4103/cjhr.cjhr_79_17

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Hunter's Syndrome or mucopolysaccharidosis Type II is a rare metabolic disorder caused by the deficiency of lysosomal enzyme iduronate-2-sulfatase. It results in progressive accumulation of deramatan and heparan sulfates in tissues leading to a wide clinical spectrum of systemic manifestations. This is a case report of a 6-year-old boy with classical features of Hunter's Syndrome who presented with a chief complaint of multiple decayed teeth. The purpose of this case report is to highlight the role of a pediatric dentist in the management of such special children with advanced dental care.


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